Go Back Brain/18. More than one of above/Normal, Technique, Anomaly/18.183 Von Hippel Lindau/ Go to Index

Autosomal dominant phacomatosis. Associated with hemangioblastomas, clear cell renal carcinomas, pheochromocytomas, and cystadenomas.

Posterior fossa hemangioblastomas associated with cysts in 2/3's of cases. The nodule usually is on the pial side of the cyst. 1/3 of hemangioblastomas not associated with cysts.

Retinal angiomas associated with hemorrhages and retinal detachment.